⚠ Questa translaziun è vegnida generada automaticamain.

Infurmaziun medica

Malurmaziuns
craniofaccialas —
explicadas simplamain.

Infurmaziuns fidablas per persunas pertutgadas, famiglias e spezialistas.

Scuvrir dapli

Cifras davart la spalta da lavra-missella-tschiel

1 : 500–700naschiensas cun spalta – tenor regiun[1]
+20specialitads medicas implitgadas
Fitg baintractabel – cun tgira interdisciplinara tempriva
~100–120naschendas cun sfendida da lavi-göl-palà per onn en Svizra[18]

Sfendidas

Sfendidas dal
Lavi-Göl-Palà

Da la diagnosa prenatal fin l'etad adulta — cumitgà pass per pass.

Malurmaziuns dal crani

Malurmaziuns
Craniofaccialas

Orientaziun en cas da suspect, diagnosa e tractament da disturbis dal crani.

Ulteriurs temas
Per specialistas & incumbents Retschertga actuala Davart nus · SGKFC

Tge è ina sfendida dal lavi-göl-palà?

La sfendida dal lavi-göl-palà è ina da las malurmaziuns congenitas las pli frequentas da la fatscha.

Cun las pussaivladads medicas d'ozildi questas malurmaziuns pon vegnir tractadas fitg bain.

Interdisciplinar

Il tractament exigescha la collavuraziun da chirurgs maxillofacials, ortodontists, ORL, logopedists e psicologs.

Diagnosa tempriva

Schisas da liev e da palat èn savens visiblas vid l'ecografia prenatala. Schisas isoladas dal palat restan blera giada betg detectadas avant la naschiensas.

Fessura dal labber – infurmaziuns detagliadas →

Concepts da tractament & qualitad

Il tractament da sfendidas na suonda betg in protocol uniform. Concepts differents coexistan.

Tecnicas da serrada da la lavra (Fisher, Millard), timing da la serrada dal palat, protocols internaziunals (Turitg, Göteborg, Oslo), osteoplastica e mesiraziun da la qualitad ICHOM – en detagl sin ina atgna pagina.

Malurmaziuns & sindroms craniofaccials

Las malurmaziuns craniofaccialas cumprendan in vast spectrum.

FAQ – Häufig gestellte Fragen

Respostas a las dumondas pli frequentas davart fessuras dal labber e dal tschiel e malformaziuns craniofacialas – rimnadas sin nossa pagina FAQ.

Vopa tuttas las 26 dumondas →

Centers spezialids & societads professiunalas

En Svizra la presa en charta è garantida da teams interdisciplinars spezialids en ils ospitals universitars. En l'Europa ils centers son colligads en la rait ERN CRANIO.

Svizra – Centers universitars spezialids

ils suandants ospitals universitars disposen da teams interdisciplinars spezialids:

Zürich
Kraniofaziales Zentrum Zürich
Universitätsspital Zürich (USZ) / Kinderspital Zürich
Basel
Spaltzentrum Basel
Universitätsspital Basel (USB) / Universitäts-Kinderspital beider Basel (UKBB)
Bern
Klinik für Mund-, Kiefer- und Gesichtschirurgie
Inselspital, Universitätsspital Bern
Lausanne
Service de chirurgie maxillo-faciale et stomatologie
Centre hospitalier universitaire vaudois (CHUV)
Genf
Service de chirurgie maxillo-faciale
Hôpitaux universitaires de Genève (HUG)

Europa – ERN CRANIO

La rait europeica da referenza per las anomalias craniofaccialas raras (ERN CRANIO) colliescha centers spezialids da 16 naziuns europeicas.

🌐

ACPA – Internaziunal

L'American Cleft Palate-Craniofacial Association (ACPA) è la societad professiunala internaziunala principala – cun dapli che 2'200 commembers en pli che 60 pajais, dapi 1943.

acpacares.org →

📋

ICHOM Standard Set

Centers che lavuran tenor l'ICHOM Standard Set mesiran ils resultats sistematicamain en set puncts da temps definids.

ichom.org →

Dumondas & Contact

Avais Vus dumondas? Voss missagi vegn criptà da fin a fin (PGP/OpenPGP).

🔐
Criptaziun da fin a fin

Voss missagi vegn criptà en il navigatur cun PGP avant la trasmissiun.

Temp da resposta

Nus ans stgaffin da respunder en 2–5 dis da lavur.

⚠ Quest website serva exclusivamain a l'infurmaziun. Na tramettai nagins datas da pazients.

Fundaments & Litteratura

Las suandantas publicaziuns furman la basa scientifica da quest website. In clic vid ina indicaziun da funtauna en il text maina a la funtauna correspundenta – il buttun cun frizza returna a la posiziun en il text.

Directivas & standards da qualitad

  1. Allori AC, Kelley T, Meara JG, et al. A standard set of outcome measures for the comprehensive appraisal of cleft care. Cleft Palate Craniofac J. 2017;54(5):540–554.
    DOI: 10.1597/15-292

Survistas sistematicas & artitgels da survista

  1. Mossey PA, Little J, Munger RG, Dixon MJ, Shaw WC. Cleft lip and palate. Lancet. 2009;374(9703):1773–1785.
    DOI: 10.1016/S0140-6736(09)60695-4
  2. Dixon MJ, Marazita ML, Beaty TH, Murray JC. Cleft lip and palate: understanding genetic and environmental influences. Nat Rev Genet. 2011;12(3):167–178.
    DOI: 10.1038/nrg2933
  3. Rohrich RJ, Love EJ, Byrd HS, Johns DF. Optimal timing of cleft palate closure. Plast Reconstr Surg. 2000;106(2):413–421.
    DOI: 10.1097/00006534-200008000-00027 · PMID: 10946935
  4. Johnson D, Wilkie AOM. Craniosynostosis. Eur J Hum Genet. 2011;19(4):369–376.
    DOI: 10.1038/ejhg.2010.235
  5. Obwegeser JA. Maxillary and midface deformities: characteristics and treatment strategies. Clin Plast Surg. 2007 Jul;34(3):519–533.
    DOI: 10.1016/j.cps.2007.05.001 · PMID: 17692708
  6. Fell M, Phippen G, van Eeden S, et al. Analysis and Reporting of Randomized Trials in Cleft Palate Surgery: Learning from the Timing of Primary Surgery (TOPS) Trial. Cleft Palate Craniofac J. 2025;62(8):1436–1442. DOI: 10.1177/10556656241253949 · PMID: 38725271 — Basiert auf dem TOPS-Trial: Gamble C, Persson C, Willadsen E, et al. Timing of Primary Surgery for Cleft Palate. N Engl J Med. 2023;389(9):795–807.
  7. Inchingolo AD, et al. Evaluation of Surgical Protocols for Speech Improvement in Children with Cleft Palate: A Systematic Review and Case Series. Bioengineering. 2025;12(8):877. DOI: 10.3390/bioengineering12080877 · PMID: 40868390 (Open Access)

Lavurs originalas & studis clinics

  1. Wilcox AJ, Lie RT, Solvoll K, et al. Folic acid supplements and risk of facial clefts: national population based case-control study. BMJ. 2007;334(7591):464.
    DOI: 10.1136/bmj.39079.618287.0B · PMID: 17259186
  2. Fisher DM. Unilateral cleft lip repair: an anatomical subunit approximation technique. Plast Reconstr Surg. 2005;116(1):61–71.
    DOI: 10.1097/01.prs.0000169689.09479.f7
  3. Bergland O, Semb G, Abyholm FE. Elimination of the residual alveolar cleft by secondary bone grafting and subsequent orthodontic treatment. Cleft Palate J. 1986;23(3):175–205.
    PubMed: 3524418
  4. Abyholm FE, Bergland O, Semb G. Secondary bone grafting of alveolar clefts. Scand J Plast Reconstr Surg. 1981;15(2):127–140.
    DOI: 10.3109/02844318109103405 · PMID: 7031462
  5. Wilkie AOM, Slaney SF, Oldridge M, et al. Apert syndrome results from localized mutations of FGFR2 and is allelic with Crouzon syndrome. Nat Genet. 1995;9(2):165–172.
    DOI: 10.1038/ng0295-165
  6. Engel M, Berger M, Hoffmann J, et al. Midface correction in patients with Crouzon syndrome: is Le Fort III distraction osteogenesis with a rigid external distraction device the gold standard? J Craniomaxillofac Surg. 2019;47(3):420–430.
    DOI: 10.1016/j.jcms.2018.11.028 · PMID: 30642732
  7. Meling TR, Due-Tønnessen BJ, Hogevold HE, Skjelbred P, Roald B. Monobloc distraction osteogenesis in pediatric patients with severe syndromal craniosynostosis. J Craniofac Surg. 2011;22(1):101–109.
    DOI: 10.1097/SCS.0b013e3181f6c620
  8. Kreutz K, Fitze G, Blecher R, et al. Helmet therapy in deformational skull base plagiocephaly also corrects facial asymmetry and ear shift. J Craniomaxillofac Surg. 2018;46(3):354–359.
    DOI: 10.1016/j.jcms.2017.12.011
  9. Meyer-Marcotty P, Böhm H, Linz C, Blecher R, et al. Spectrum of positional deformities – is there a real difference between plagiocephaly and brachycephaly? J Craniomaxillofac Surg. 2014;42(6):1010–1016.
    DOI: 10.1016/j.jcms.2014.01.026 · PMID: 24530071
  10. Ferrari R, Özcan M, Wiedemeier D, Essig H. Accuracy of intraoral scanners in the cleft anatomy of neonates. Int J Comput Dent. 2025 Sep 1;28(3):225–234.
    DOI: 10.3290/j.ijcd.b5886430 · PMID: 39871769
  11. Bezuhly M, Fisher DM. Single-stage repair of asymmetrical bilateral cleft lip with contralateral lesser form defects. Plast Reconstr Surg. 2012;129(3):751–757.
    DOI: 10.1097/PRS.0b013e3182402f50

Datas epidemiologicas & infurmaziuns per pazients

  1. Berechnet aus: Bundesamt für Statistik (BFS). Statistik der natürlichen Bevölkerungsbewegung (BEVNAT) – Lebendgeburten Schweiz, ca. 85 000/Jahr. Neuchâtel: BFS, 2023. Kombiniert mit europäischer Prävalenz orofazialer Spalten (ca. 1 : 700; EUROCAT Registry: eu-rd-platform.jrc.ec.europa.eu/eurocat) → ca. 100–120 Neugeborene mit LKG-Spalte jährlich in der Schweiz. Übereinstimmend: Kaiser G, Thüer U, Scheurer Ph. Lippen-Kiefer-Gaumenspalten – Informationsschrift für Eltern. 3. Aufl. Bern: Inselspital / Universität Bern, 2000.

Impressum & Protecziun da datas

Responsabel per il cuntegn da quest website

E-mail: kontakt@kraniofazial.ch

Exclusiun da responsabladad

Quest website serva exclusivamain a l'infurmaziun. Il cuntegn na remplazza nagina cussegliaziun u diagnosa mediala.

Contact

kontakt@kraniofazial.ch

Decleraziun da protecziun da datas

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Voss dretgs

Infurmaziun, correcziun e stritgamaint da vossas datas: kontakt@kraniofazial.ch

Remartga: Il cuntegn da questa pagina serva a l'infurmaziun generala e na remplazza betg in cussegl medicinal individual, ina diagnosa u in tractament. Las indicaziuns davart la surpigliada dals custs tras las assicuranzas n'èn betg liantas; decisiv è il giudicament dal cas singul tras l'assicuranza cumpetenta. Per dumondas As drizzai al Voss team da tractament.